REGULAR CONTENT
Final ID
584
Type
Educational Exhibit-Poster Only
Authors
J Koo1, J Hazelton2, M Pasyk3, G Elias3, J Tisnado3
Institutions
1Wayne State University School of Medicine / Detroit Medical Center, Detroit, MI, 2Wayne State University School of Medicine, Detroit, MI, 3Virginia Commonwealth University, Richmond, VA
Purpose
To review the pathophysiology, clinical presentation, radiologic diagnosis and therapeutic management of mid aortic syndrome in children.
Materials & Methods
Mid aortic syndrome (MAS) is a rare cause of hypertension in children. It is characterized by significant stenosis of the mid abdominal aorta and is frequently associated with concomitant involvement of visceral (celiac and superior mesenteric) and renal arteries. The etiology of MAS is unclear and controversial.
Results
Depending upon the site of vascular stenosis, the child may be asymptomatic or may present with uncontrollable hypertension with or without renal failure. Other clinical manifestations include lower limb claudication, headache, epistaxis, chest pain, cardiac failure and abdominal pain. If left untreated, MAS is associated with significant morbidity and mortality. Diagnostic images of MAS with Doppler ultrasonography, contrast-enhanced CT, and MRI are presented. Each imaging modality is correlated with the patient's clinical presentation and diagnosis.The indications for treatment, timing, and rationale for various management strategies are discussed. The traditional therapeutic intervention is open surgical reconstruction with bypass grafting, however, depending upon the nature of the vascular involvement, percutaneous angioplasty with or without stenting may be performed. Finally, the specific procedural details and the goals of therapeutic options are reviewed.
Conclusions
Radiologic evaluation is critical for the diagnosis and development of patient-specific treatment strategy. Both, traditional open surgical bypass and newer endovascular techniques may be employed during the management of mid aortic syndrome. Open surgery is the primary treatment of choice, however, endovascular intervention may provide a safe and less invasive treatment option for patients with mid aortic syndrome.
Final ID
584
Type
Educational Exhibit-Poster Only
Authors
J Koo1, J Hazelton2, M Pasyk3, G Elias3, J Tisnado3
Institutions
1Wayne State University School of Medicine / Detroit Medical Center, Detroit, MI, 2Wayne State University School of Medicine, Detroit, MI, 3Virginia Commonwealth University, Richmond, VA
Purpose
To review the pathophysiology, clinical presentation, radiologic diagnosis and therapeutic management of mid aortic syndrome in children.
Materials & Methods
Mid aortic syndrome (MAS) is a rare cause of hypertension in children. It is characterized by significant stenosis of the mid abdominal aorta and is frequently associated with concomitant involvement of visceral (celiac and superior mesenteric) and renal arteries. The etiology of MAS is unclear and controversial.
Results
Depending upon the site of vascular stenosis, the child may be asymptomatic or may present with uncontrollable hypertension with or without renal failure. Other clinical manifestations include lower limb claudication, headache, epistaxis, chest pain, cardiac failure and abdominal pain. If left untreated, MAS is associated with significant morbidity and mortality. Diagnostic images of MAS with Doppler ultrasonography, contrast-enhanced CT, and MRI are presented. Each imaging modality is correlated with the patient's clinical presentation and diagnosis.The indications for treatment, timing, and rationale for various management strategies are discussed. The traditional therapeutic intervention is open surgical reconstruction with bypass grafting, however, depending upon the nature of the vascular involvement, percutaneous angioplasty with or without stenting may be performed. Finally, the specific procedural details and the goals of therapeutic options are reviewed.
Conclusions
Radiologic evaluation is critical for the diagnosis and development of patient-specific treatment strategy. Both, traditional open surgical bypass and newer endovascular techniques may be employed during the management of mid aortic syndrome. Open surgery is the primary treatment of choice, however, endovascular intervention may provide a safe and less invasive treatment option for patients with mid aortic syndrome.